Isolated Non-Compacted Myocardium: Should We Consider the Presence of Extrasystoles as the Initial Manifestation?

Abstract Ventricular non-compaction occurs due to failure in myocardial morphogenesis during the fetal period. Patients can have heart failure, as well as systemic complications due to thromboembolism and cardiac arrhythmias. Early diagnosis is essential. We present the case of an asymptomatic 49-year-old woman who initially manifested ventricular extrasystoles and heart failure with reduced ejection fraction and a myocardial noncompaction diagnosis.

摘要：心室非致密化心肌病（Ventricular non-compaction）由胎儿期心肌形态发生障碍所引发。患者可出现心力衰竭，亦可因血栓栓塞与心律失常引发全身并发症，早期诊断至关重要。本文报告1例无症状的49岁女性患者，其初始临床表现为室性期前收缩、射血分数降低型心力衰竭，最终确诊为心肌非致密化病变。