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Clinical characteristics of family members according to LMNA mutation carrier status.

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Figshare2015-12-03 更新2026-04-29 收录
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Mean values ± standard deviation or absolute frequencies and percentage of patients.AF = atrial fibrillation; AVB = atrioventricular block; BMI = body mass index; CMRI = cardiac magnetic resonance imaging; DBP = diastolic blood pressure; Echo = echocardiography; LGE = late gadolinium enhancement; LVEDD = left ventricular end-diastolic diameter; LVEF = left ventricular ejection fraction; NSVT = non-sustained ventricular tachycardia; PVCs = premature ventricular complexes; RVEF = right ventricular ejection fraction; RVOT = right ventricular outflow tract; SBP = systolic blood pressure; SVT = sustained ventricular tachycardia.*RVOT value by echocardiography was available in 19 of 20 patients, 9 of whom were LMNA mutation-positive subjects.†CMRI was performed in 15 subjects, 7 of whom were LMNA mutation carriers.Clinical characteristics of family members according to LMNA mutation carrier status.
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2015-12-03
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