Outcome measures for 30–33 week old omigapil and vehicle treated dy2J mice after 17.5 weeks show significant improvements in respiratory rate and fibrosis in dy2J 0.1 mg/kg omigapil treated mice.

*Non-parametric comparison of medians; data expressed as mean ± SD; median (range).Abbreviations: %FS – percent fractional shortening, %EF- percent ejection fraction, BPM- beats per minute, bpm – breaths per minute, SD – standard deviation, PA – pulmonary artery, AO – aortic, E/A – ratio of mitral valve E and A wave velocities, GSM – grip strength meter, BW- body weight, Gastroc – gastrocnemius, TA – tibialis anterior, KGF.