Residual enzyme activities of mitochondrial respiratory chain complexes in different tissues from the index patient.
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Enzyme activities are expressed as*cU/U citrate synthase (CS) and**nmol.min−1.mg prot−1. CS activity is expressed as mU/mg protein. Abnormal values are indicated in bold. nd, not determined. Complex I, CI; Complex II, CII; Complex III, CIII; Complex IV, CIV.
创建时间:
2015-12-02



