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Residual enzyme activities of mitochondrial respiratory chain complexes in different tissues from the index patient.

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Figshare2015-12-02 更新2026-04-29 收录
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Enzyme activities are expressed as*cU/U citrate synthase (CS) and**nmol.min−1.mg prot−1. CS activity is expressed as mU/mg protein. Abnormal values are indicated in bold. nd, not determined. Complex I, CI; Complex II, CII; Complex III, CIII; Complex IV, CIV.
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2015-12-02
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