Supplementary Material for: Unilateral Congenital Lenticular Pigmentation

Introduction Release of pigments in the anterior chamber is frequently observed in Pigment Dispersion Syndrome (PDS), an autosomal dominant disorder marked by bilateral pigment deposition on the anterior and possibly posterior lens capsule, zonules of the lens, trabecular meshwork, and corneal endothelium, in addition to radial, spoke-like trans-illumination defects in the mid peripheral iris [1,4]. Pigmentation of the anterior lens surface has also been associated with intraocular inflammation, pseudoexfoliation syndrome, siderosis, antipsychotic medication usage, and remnants of the tunica vasculosa lentis [2]. Case presentation A 23 years old female presented to our Eye clinic with chief complaint of mild blurring of vision in the right eye and enquiring about refractive surgery. The patient denied any previous history of ocular inflammation, trauma, surgery, or use of topical or systemic medications. Slit lamp examination of the right eye anterior segment was within normal limit except for the crystalline lens anterior capsular which showed confluent pigment deposits stellate in shape over the pupillary axis whereas left eye examination was completely within normal limit. Ophthalmic examination of the posterior segment was normal in both eyes. Based on her previous ophthalmic history and slit-lamp examination of the right eye a diagnosis of unilateral congenital lenticular pigmentation was made. Conclusion Congenital lenticular pigmentation is a rare benign entity carrying no surgical indications with a relatively good visual response to optical correction. Recognition of this rare benign condition would add to the Ophthalmologist's differential of ocular pigmentation and avoid unnecessary concern and follow up in more potentially progressive disorders such as pigmentary glaucoma.