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Modern Approach to Cardiological Monitoring in H63D Syndrome incl. Oshtoran Syndrome

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DataCite Commons2025-01-16 更新2025-04-15 收录
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https://dataverse.harvard.edu/citation?persistentId=doi:10.7910/DVN/ULAQMJ
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Data Content Traditional calendar-based cardiological monitoring presents significant limitations in H63D Syndrome due to its complex pathophysiology, including NTBI overload, autonomic dysfunction, and inappropriate catecholamine release. This guideline presents a modernized monitoring approach based on accumulated clinical experience. It introduces a flexible, patient-centered strategy combining home-based diagnostic tools with quarterly clinical reviews. The approach emphasizes the importance of manual verification in complex measurements and establishes clear trigger points for additional evaluation. This adaptive monitoring system maintains high standards of care while reducing iatrogenic stress and improving resource utilization. The guideline provides practical implementation strategies for transitioning from fixed-interval to adaptive monitoring while preserving the physician-patient relationship.
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Harvard Dataverse
创建时间:
2025-01-16
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