Uterine tumor resembling ovarian sex cord tumor - a rare gynecological neoplasm

Uterine tumor resembling ovarian sex cord tumor (UTROSCT) is a rare group of uterine neoplasms with unknown histogenesis and differentiation towards ovarian sex cord elements. They are benign in nature with low malignancy potential. Diagnosis is based on immunohistochemistry and morphological features and the distinction from other more malignant differentials is paramount to individualize treatment correctly. UTROSCT is a rare gynecological entity with no established treatment protocol. Differentiation between benign and malignant behavior is based on structural features and immunohistochemical expression assessment. This highlights the importance of immunohistochemical staining and morphological analysis to determine the degree of surgical radicality. Minimally invasive approach is feasible and safe, but more experience is needed for further conclusions.