CoQ<sub>10</sub> biosynthesis pathway.
收藏NIAID Data Ecosystem2026-03-06 收录
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资源简介：
CoQ10 is composed of a benzoquinone and a decaprenyl side chain. PDSS2 is the second subunit of decaprenyl diphosphate synthase, a heterotretameric enzyme that catalyzes the formation of the decaprenyl side chain. COQ2 or para-hydroxybenzoate (PHB)-polyprenyl transferase catalyzes the condensation reaction of PHB and decaprenyl diphosphate. The function of COQ9 is still unknown. The mutant fibroblasts used in this study harbor mutations in COQ9, p.244R>X (P1) [18], COQ2, p.197R>H, p.228N>S (P2) [14] and p.297Y>C (P3) [17], and PDSS2, p.322Q>X, p.382S>L (P4) [20].
创建时间：
2016-02-24
