Osteogenesis imperfecta (OI) patients' pulmonary function test.

Data are expressed as mean±standard deviation. FVC: forced vital capacity;1Reference values from Quanjer et al, 1993;2Reference values from Kuster et al, 2008; FEV1: forced expiratory volume in 1 s; TLC: total lung capacity; RV: residual volume; FRC N2: functional residual capacity measured by N2 washout; SpO2: arterial oxygen saturation measured by pulse oxymetry; %pred: percentage of predicted value.°,°°p