Clinical characteristics of the nine MODY probands investigated.

None of the individuals had hearing loss or acantosis nigricans. Data regarding hepatic steatosis, renal cysts, polycystic ovarian disease and triglyceride status were not available in all individuals.aP01 also had partial lipodystrophy with reduced subcutaneous fat in extremities and excess of abdominal subcutaneous fat. There was no evidence of hypertriglyceridemia, hepatic steatosis, acanthosis nigricans or polycystic ovarian disease.bAn affected family member was diagnosed at age 28 years.Abbreviations: BMI, body mass index; DM, diabetes mellitus; NA, not available; OHA, Oral Hypoglycemic agents; U, international unit (used for insulin doses); y, year; kg, kilo gram body weight.