Alterations of skeletal muscle bioenergetics in a mouse with F508del mutation leading to a cystic fibrosis-like condition
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Figure 1S. State 4 respiratory rates of skeletal muscle subsarcolemmal (a) and interfibrillar (b) mitochondria in presence of mitochondria substrates for: complex I (malate and glutamate, G<sub>M</sub>), (malate and pyruvate, P<sub>M</sub>); complex II (succinate and rotenone, S<sub>R</sub>); complex III (duroquinol and rotenone, (DHQ<sub>R</sub>); complex IV (TMPD, ascorbate and rotenone, TMPD+A)<sub>R</sub>. * p<0.05 WT (n=6) vs. CF (n=7), Mean ± standard deviation. Figure 2S. The ratio ADP to atomic oxygen phosphorylation (ADP/O) of skeletal muscle SSM (a) and IFM (b) in CF and WT mice. Complex I (malate and glutamate, G<sub>M</sub>; malate and pyruvate, P<sub>M</sub>); complex II (succinate and rotenone, S<sub>R</sub>); complex III (duroquinol and rotenone, (DHQ<sub>R</sub>). * p<0.05 WT (n=6) vs. CF (n=7), Mean ± standard deviation.
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2019-06-11



