Patients' characteristics (n = 21).

Values are n or mean (SD). * Includes two patients with Eisenmenger physiology related to persistent arterial canal and ventricular septal defect. ** Right heart catheterization performed <6 months was used to describe hemodynamic severity. Table legend: PAH, Pulmonary arterial hypertension; IPAH, Idiopathic PAH; PAH-Her, Heritable PAH; PAH-CTD, PAH associated with connective tissue disease; PAH-CHD, PAH associated with congenital heat disease; BMI, Body mass index; WHO, World Health Organization; RAP, Right atrial pressure; mPAP, Mean pulmonary artery pressure; PCWP, Pre-capillary wedge pressure; CI, Cardiac index; PVRi, Pulmonary vascular resistance index; 6MWD, six-minute walk distance.