Clinical data of the study population.

Total values are presented as median with interquartile range. * Missing data (4 cases) a percentage with exocrine insufficiency b percentage with CFRD c percentage with pseudomonas colonization IN-950 CT emphysema quantified as the percentage of voxels below -950HU in inspiration FEV1 Forced expiratory volume in the first second; FEV1/FVC ratio of FEV1 over forced vital capacity; MEF25–75 Mean flow between 25% and 75% of forced vital capacity; CFRD cystic fibrosis related diabetes. Clinical data of the study population.