Activities of oxidative phosphorylation enzyme complexes in patient and control lymphoblast cell lines.

Mitochondrial complex I activity was taken as the one that is rotenone sensitive. Specific enzyme activities shown as nmol/min/mg protein. I; NADH-DB oxidoreductase, II; Succinate-DB oxidoreductase, II+III; Succinate Cytochrome C reductase, IV; Cytochrome C oxidase, CS; Citrate synthase. ** and * indicate P values that are stastically significant (p