Surgical Repair of Complex Aortopulmonary Window: A Case Study

Abstract Aortopulmonary septal defect, also known as the aortopulmonary window, is a rare congenital macrovascular malformation. This case involves a 9-year-old boy with aortopulmonary septal defect (type I combined with type IV). Before surgery, milrinone and alprostadil were used to counteract high lung pressure. Surgery was performed under cardiopulmonary bypass, following which the pulmonary pressure decreased. The aorta was cut, and the right pulmonary artery opening was connected with the main pulmonary artery septal defect using polyester patch. An internal tunnel was made, and the deformity correction was completed. The child exhibited normal postoperative recovery with no discomfort. A complex aortopulmonary window is a rare condition that can be treated successfully with appropriate preoperative and surgical management.摘要 主肺动脉间隔缺损（aortopulmonary septal defect），又称主肺动脉窗（aortopulmonary window），是一种罕见的先天性大血管畸形。本病例涉及1名9岁男性主肺动脉间隔缺损患者（Ⅰ型合并Ⅳ型）。术前使用米力农与前列地尔以对抗肺动脉高压。手术在体外循环下进行，术后患者肺动脉压下降。术中切开主动脉，以涤纶补片将右肺动脉开口与主肺动脉间隔缺损处进行吻合，并构建内部隧道，完成畸形矫治。患儿术后恢复良好，无不适症状。复杂型主肺动脉窗为罕见病症，经恰当的术前管理与手术治疗可获得成功预后。