Clinical characteristics of family members according to <i>LMNA</i> mutation carrier status.
收藏资源简介:
Mean values ± standard deviation or absolute frequencies and percentage of patients. AF = atrial fibrillation; AVB = atrioventricular block; BMI = body mass index; CMRI = cardiac magnetic resonance imaging; DBP = diastolic blood pressure; Echo = echocardiography; LGE = late gadolinium enhancement; LVEDD = left ventricular end-diastolic diameter; LVEF = left ventricular ejection fraction; NSVT = non-sustained ventricular tachycardia; PVCs = premature ventricular complexes; RVEF = right ventricular ejection fraction; RVOT = right ventricular outflow tract; SBP = systolic blood pressure; SVT = sustained ventricular tachycardia. *RVOT value by echocardiography was available in 19 of 20 patients, 9 of whom were LMNA mutation-positive subjects. †CMRI was performed in 15 subjects, 7 of whom were LMNA mutation carriers. Clinical characteristics of family members according to LMNA mutation carrier status.
本数据集以均值±标准差或绝对频数及患者占比的形式呈现相关数据。 各缩写释义如下: AF:心房颤动(atrial fibrillation);AVB:房室传导阻滞(atrioventricular block);BMI:体质量指数(body mass index);CMRI:心脏磁共振成像(cardiac magnetic resonance imaging);DBP:舒张压(diastolic blood pressure);Echo:超声心动图(echocardiography);LGE:晚期钆增强(late gadolinium enhancement);LVEDD:左心室舒张末期内径(left ventricular end-diastolic diameter);LVEF:左心室射血分数(left ventricular ejection fraction);NSVT:非持续性室性心动过速(non-sustained ventricular tachycardia);PVCs:室性期前收缩(premature ventricular complexes);RVEF:右心室射血分数(right ventricular ejection fraction);RVOT:右心室流出道(right ventricular outflow tract);SBP:收缩压(systolic blood pressure);SVT:持续性室性心动过速(sustained ventricular tachycardia)。 * 经超声心动图检测的右心室流出道(RVOT)数值在20例患者中共有19例可获取,其中9例为LMNA突变阳性受试者。 † 共15例受试者接受了心脏磁共振成像(CMRI)检查,其中7例为LMNA突变携带者。 本数据集呈现了根据LMNA突变携带状态划分的家庭成员临床特征。




